Post-translational modifications of proteins by lipids; neuronal ceroid lipofuscinosis

Place of work — Department of Internal
Medicine, Hamon Center
for Therapeutic Oncology
Research, University of
Texas, USA
Contacts — 5323 Harry Hines Blvd. Dallas, TX 75390–9003, USA (214) 648–4900 sandra.hofmann@utsouthwestern.edu
Publications — Thematic review series: lipid posttranslational modifications. Lysosomal metabolism of lipid- modified proteins. Lu JY, Hofmann SL. J Lipid Res. 2006 Jul;47(7):1352–7.
Inefficient cleavage of palmitoyl-protein thioesterase (PPT) substrates by aminothiols: implications for treatment of infantile neuronal ceroid lipofuscinosis. Lu JY, Hofmann SL. J Inherit Metab Dis. 2006 Feb;29(1):119–26.
Functional biology of the neuronal ceroid lipofuscinoses (NCL) proteins. Kyttälä A, Lahtinen U, Braulke T, Hofmann SL. Biochim Biophys Acta. 2006 Oct;1762(10):920–33.